Unfortunately there is currently no cure for pulmonary fibrosis and there is limited treatment available. Using an oxygen tank can help manage the strain of Pulmonary Fibrosis, however this varies from case to case and you should consult your doctor to learn more.
Recent research data also suggests a potential role for several therapies for people with IPF. Please see below for more information.
- Pirfenidone – Esbriet™ (pirfenidone) is an anti-fibrotic/anti-inflammatory agent approved by Health Canada for the treatment of mild to moderate idiopathic pulmonary fibrosis in adults.
- N-Acetylcysteine (NAC) – One research study found that adding N-acetylcysteine (NAC) to traditional prednisone-containing therapies may be helpful, but it is not clear how helpful this drug is when used on its own. N-acetylcysteine (NAC) is available over the counter at many pharmacies and nutritional stores and has very few side effects.
- Prednisone plus Azathioprine – Combining two medications, such as Prednisone and a second drug such as Azathioprine (or Mycophenolate and Cyclophosphamide), has been used for the treatment of IPF.
Your doctor will talk to you about which, if any, of these treatments may be right for you.
The Canadian Pulmonary Fibrosis Foundation is supporting the University Health Network’s Interstitial Lung Diseases Clinic at Toronto General Hospital with a research grant for their Idiopathic Pulmonary Fibrosis and Gastroesophageal Reflux Disease research project. Read more…
Currently a lung transplant is the only effective treatment for Pulmonary Fibrosis. The Multi Organ Transplant Program at Toronto General Hospital can be consulted regarding lung transplants.
Please visit the University Health Network to find out more about the internationally renown Multi-Organ Transplant Program